Pulmonary fibrosis refers to a lung disease which results in scarring of the lungs. It becomes difficult to breathe as well as get sufficient oxygen. Scarring continues to get worse over time and can disrupt an individual’s daily routine.
There is no cure for the disease, but it can significantly improve in well diagnosed and treated patients.
This article focuses on the diagnostic methods of pulmonary fibrosis, treatment options, and disease management in daily life.
A Closer Look at the Disease
Pulmonary fibrosis occurs as a result of damage and scarring of the lungs. The scar formation results in stiff lung tissues which makes it very difficult for oxygen to pass into the blood. It becomes highly difficult to breathe deeply or perform physical activities.
In some instances, doctors remain unsure of the underlying causes. In this scenario, it is referred to as Idiopathic Pulmonary Fibrosis (IPF). A few other causes may involve:
- Exposure to dust, smoke, or chemicals
- Autoimmune disease: lupus or rheumatoid arthritis
- Radiation therapy (most common for cancer care)
- Specific medicines like chemotherapy, heart medicine, or medicinal drugs
Risk Factors
Some individuals have higher chances of getting pulmonary fibrosis. These are known as risk factors, and include:
Age: Mostly prevalent in patients older than 50 years of age
Gender: Slightly more prevalent in males
Smoking: Greater lung damage with time
Occupational exposure: Mining, farming, and construction
Family: Positive family history of lung disease
Medical: Autoimmune diseases like Scleroderma or Sarcoidosis
All these risks aid both the patient and the doctor in making an early diagnosis in case the disease progresses.
Diagnosis Methods
Diagnosis of pulmonary fibrosis tends to be more time-consuming and arrives at a clear conclusion to identifying the disease step-by-step. Some steps include:
Medical History
A doctor inquires about an illness previous to that and one’s occupation including smoking and exposure to dust or chemicals. Family diseases are also considered.
Auscultation (of the lungs)
Doctors listen to the lungs using a stethoscope. If scarring took place, crackling noise may be present.
Imaging Tests Chest X-ray
Describes if damage or scarring has occurred in the lungs.
High-Resolution CT Scan: Provides clearer, more intricate pictures of the lungs.
Breathing Tests
These tests evaluate pulmonary function. They determine the amount of air exhaled and the amount of oxygen consumed.
Spirometry Lung volume test Diffusing capacity test
Oxygen Tests Pulse oximeter (placed on your finger) helps check if oxygen levels are suboptimal. Blood samples might also be taken. Blood Tests Helps in excluding other conditions such as infections and autoimmune conditions.
Lung Biopsy
At times, examiners require visual analysis of pulmonary tissues under a microscope. This procedure can be performed through a bronchoscope or surgically if deemed necessary.
Treatment Options
There is no cure for pulmonary fibrosis but treatment can help in managing it. Its main aim is to alleviate symptoms, limit complications, and improve breathing.
Medications
Pirfenidone (Esbriet)
This drug may increase the quality of life of a patient with lung scarring while also potentially increasing life expectancy. Patient care programs can help lower the high Pirfenidone price, and insurance support often makes it more affordable.
Corticosteroids (like Prednisone)
Inflammation of the lungs is a common problem, and Prednisone helps alleviate this. It’s also very cost effective and available at a low Prednisone price.
Nintedanib (Ofev)
Nintedanib treats lung scarring caused by a fibrosis disease by restricting some scar tissue generating proteins. Though the Nintedanib price is fairly expensive, it does have some saving plans.
Azathioprine
Immunosuppressant’s such as Azathioprine work sometimes with steroids. The general price of Azathioprine is low and often included in several health insurance plans.
Oxygen Therapy
Oxygen assists the body when the lungs cannot provide enough on their own. It can be applied:
- During Exercise
- Night time
- Throughout the day for extreme conditions
- This therapy improves energy and helps with breathlessness.
Pulmonary Rehabilitation
This is a unique course that shows patients how to stay active and exercise to achieve better oxygen flow. It often features:
- Breathing Techniques
- Mild Aerobic Exercises
- Diet and health guidance
- Mental health care counselling
Lung Transplant
A lung transplant is required in more severe instances. The operation involves replacing damaged lungs with healthy lungs obtained from a donor. Hospitals specializing in this surgery include the Cleveland Clinic and the Mayo Clinic. Transplants enhance breathing abilities, as well as life expectancy.
Healthy Habits Matter
It is crucial to take care of your health when you are living with pulmonary fibrosis. Here are some suggestions that would help:
No smoking: Smoking is detrimental to the lungs.
Stay active: Walking or performing light exercises can keep the lungs active.
Healthy eating: Healthy diet helps fight infections. Consume vegetables, fruits, and lean proteins.
Get good rest: Helps your body recover.
Wash hands: These practices keep sick peers at bay
Get Vaccinated: It is key to get vaccinated for flu and pneumonia for those living with any respiratory condition.
Monitoring the Disease
Doctors will continuously monitor your condition to ascertain if it is worsening or improving. Follow up visits may include, but not limited to:
- Tests to ascertain lung functionality. Oxygen levels assessment. Chest scans. Blood tests.
- Keeping up with these appointments allows you to fine-tune your treatment plan if need be.
Hope of Better Treatment
Scientists are working endlessly on methods to treat or even reverse scarring for pulmonary fibrosis. Several hospitals and research centers have come up with clinical trials which allow patients access to experimental treatments prior to widespread availability.
Genentech and Boehringer Ingelheim are some of the companies working to develop better alternatives. Future care also includes promising prospects with stem cell therapy and gene research.
Conclusion
Pulmonary fibrosis is a life threatening disease that alters the mechanics of breathing. The damage done to the lungs makes oxygen supply difficult which can lead to fatigue and shortness of breath. Even so, early diagnosis with medication, oxygen, and rehab allows people to live a meaningful life. Regular check-ups along with new treatments and healthy living improve the lives of patients suffering from this condition.
